DiseaseID 3689
获得性低丙种球蛋白血症
disease
Common variable immunodeficiency (CVID) comprises a heterogeneous group of diseases characterized by a significant hypogammaglobulinemia of unknown cause, failure to produce specific antibodies after
Relationship Network
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Disease: 1Formula: 5Herb: 2Symptom: 12Target: 24Links: 43
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Record Fields
Scalar fields from the final disease record.
- Disease Id
- 3689
- Core Entity Id
- 59925
- Source Entity Count
- 1
- Preferred Name
- Acquired Hypogammaglobulinemia
- Name Cn
- 获得性低丙种球蛋白血症
- Name Pinyin
- Huo De Xing Di Bing Zhong Qiu Dan Bai Xue Zheng
- Name En
- Acquired Hypogammaglobulinemia
- Name Latin
- Bilingual Status
- complete
- Disease Type
- disease
- Umls Disease Type
- Disease or Syndrome
- Disgenet Type
- disease
- Mesh Class
- Immune System DiseasesImmune System Diseases; Congenital, Hereditary, and Neonatal Diseases and Abnormalities
- Do Class
- disease of anatomical entity
- Hpo Class
- Mesh Class Name
- Immune System Diseases
- Hpo Class Name
- Do Class Name
- disease of anatomical entity
- Disease Definition
- Common variable immunodeficiency (CVID) comprises a heterogeneous group of diseases characterized by a significant hypogammaglobulinemia of unknown cause, failure to produce specific antibodies after
- Version
- v1
- Suppressed
- No
Names
Preferred names, aliases, and source labels retained in the final schema.
Name
Acquired Hypogammaglobulinemia
Role
preferred
Name
Common Variable Immunodeficiency
Role
preferred
Name
Immunodeficiency, Common Variable, 1
Role
preferred
Name
Immunodeficiency, Common Variable, 11
Role
preferred
Name
Immunodeficiency, Common Variable, 2
Role
preferred
Name
Immunodeficiency, Common Variable, 4
Role
preferred
Name
Immunodeficiency, Common Variable, 5
Role
preferred
Name
Immunodeficiency, Common Variable, 6
Role
preferred
Name
Immunodeficiency, Common Variable, 7
Role
preferred
Name
Immunodeficiency, Common Variable, 8, With Autoimmunity
Role
preferred
Name
Antibody Deficiency Due To Defect In Cd19
Role
preferred
Name
IMMUNODEFICIENCY, COMMON VARIABLE, 10
Role
preferred
Name
Immunoglobulin Deficiency, Late-Onset
Role
preferred
Name
ANTIBODY DEFICIENCY DUE TO BAFFR DEFECT
Role
alias
Name
ANTIBODY DEFICIENCY DUE TO CD20 DEFECT
Role
alias
Name
ANTIBODY DEFICIENCY DUE TO CD81 DEFECT
Role
alias
Name
ANTIBODY DEFICIENCY DUE TO ICOS DEFECT
Role
alias
Name
ANTIBODY DEFICIENCY DUE TO TACI DEFECT
Role
alias
Name
Antibody Deficiency Due To Cd19 Defect
Role
alias
Name
CVID
Role
alias
Name
CVID1
Role
alias
Name
CVID11
Role
alias
Name
CVID2
Role
alias
Name
CVID4
Role
alias
Name
CVID5
Role
alias
Name
CVID6
Role
alias
Name
CVID7
Role
alias
Name
CVID8
Role
alias
Name
Common Variable Immunodeficiency, Unspecified
Role
alias
Name
HYPOGAMMAGLOBULINEMIA DUE TO TACI DEFICIENCY
Role
alias
Name
IL21 DEFICIENCY
Role
alias
Name
IMMUNODEFICIENCY, COMMON VARIABLE
Role
alias
Name
Idiopathic Immunoglobulin Deficiency
Role
alias
Name
Immunodeficiency, Common Variable, 3
Role
alias
Name
Primary Antibody Deficiency
Role
alias
Name
Primary Hypogammaglobulinemia
Role
alias
Cross References
Trusted external identifiers retained for this final record.
Herb
HBDIS000632HBDIS020423HBDIS020424HBDIS020600HBDIS020628HBDIS020672HBDIS020673HBDIS021761HBDIS022395HBDIS023004HBDIS029256HBDIS029257HBDIS029376
Me Sh
D017074
Omim
240500607594613493613494613495613496614699614700615577615767
Umls
C0009447C2936664C3149378C3150354C3150739C3150740C3150741C3542922C3553512C3809991C4014258
Icd10
D83D83.9
Sym Map
SMDE00644SMDE02096SMDE02121SMDE03174SMDE03910SMDE04387SMDE04398SMDE04606SMDE04987SMDE05034SMDE05370
Do Class
DOID:7
Dis Ge Net
C0009447C2936664C2936665C3149378C3150354C3150738C3150739C3150740C3150741C3542922C3553512C3809991C4014258
Orphanet
1572
Umls Sty
T047
Me Sh Class
C16C20
Etcm Disease
Common Variable ImmunodeficiencyImmunodeficiency, Common Variable, 1Immunodeficiency, Common Variable, 10Immunodeficiency, Common Variable, 11Immunodeficiency, Common Variable, 2Immunodeficiency, Common Variable, 4Immunodeficiency, Common Variable, 5Immunodeficiency, Common Variable, 6Immunodeficiency, Common Variable, 7Immunodeficiency, Common Variable, 8, with Autoimmunity
Tcmbank Disease
1194412124123051316716777189182005828197316873764
Itcmdb Generated
ITX-DISEASE-2A677207139DITX-DISEASE-45C1C761AC6CITX-DISEASE-4A808E615621ITX-DISEASE-5EAF00505D97ITX-DISEASE-635A445CF4C9ITX-DISEASE-6C03D164AE0DITX-DISEASE-71E4422A0BCAITX-DISEASE-7C693FF06029ITX-DISEASE-8E7AD43531B8ITX-DISEASE-9087D2A75EC9ITX-DISEASE-909567FC07EFITX-DISEASE-92D0B054A9C8ITX-DISEASE-93E263CBE8F7ITX-DISEASE-AC185717D8ADITX-DISEASE-C013A2A3F747ITX-DISEASE-CF21328575C1ITX-DISEASE-FFA82E6F4FFA
Attributes
Merged source attributes and domain-specific metadata.
Version
v1v1,v2v2
Suppress
0
Page Title
Disease Common Variable Immunodeficiency Details pageDisease Immunodeficiency, Common Variable, 1 Details pageDisease Immunodeficiency, Common Variable, 10 Details pageDisease Immunodeficiency, Common Variable, 11 Details pageDisease Immunodeficiency, Common Variable, 2 Details pageDisease Immunodeficiency, Common Variable, 4 Details pageDisease Immunodeficiency, Common Variable, 5 Details pageDisease Immunodeficiency, Common Variable, 6 Details pageDisease Immunodeficiency, Common Variable, 7 Details pageDisease Immunodeficiency, Common Variable, 8, with Autoimmunity Details page
Do Class Name
disease of anatomical entity
Disease Type
disease
Do Disease Class
disease of anatomical entity
Umls Disease Type
Disease or Syndrome
Basic Information
Disease Name
Common Variable Immunodeficiency
Global Category
Rare diseases
Anatomical Category
Blood diseases;Immune diseases
Disease Name
Immunodeficiency, Common Variable, 1
Global Category
Genetic diseases
Anatomical Category
Immune diseases
Disease Name
Immunodeficiency, Common Variable, 10
Global Category
Genetic diseases;Rare diseases
Anatomical Category
Blood diseases;Endocrine diseases;Immune diseases
Disease Name
Immunodeficiency, Common Variable, 11
Global Category
Genetic diseases;Rare diseases
Anatomical Category
Blood diseases;Gastrointestinal Diseases;Immune diseases
Disease Name
Immunodeficiency, Common Variable, 2
Global Category
Genetic diseases
Anatomical Category
Immune diseases
Disease Name
Immunodeficiency, Common Variable, 4
Global Category
Genetic diseases
Anatomical Category
Immune diseases
Disease Name
Immunodeficiency, Common Variable, 5
Global Category
Genetic diseases
Anatomical Category
Immune diseases
Disease Name
Immunodeficiency, Common Variable, 6
Global Category
Genetic diseases
Anatomical Category
Immune diseases
Disease Name
Immunodeficiency, Common Variable, 7
Global Category
Genetic diseases
Anatomical Category
Immune diseases
Disease Name
Immunodeficiency, Common Variable, 8, with Autoimmunity
Global Category
Genetic diseases;Rare diseases
Anatomical Category
Blood diseases;Endocrine diseases;Gastrointestinal Diseases;Immune diseases
Disease Definition
Common variable immunodeficiency (CVID) comprises a heterogeneous group of diseases characterized by a significant hypogammaglobulinemia of unknown cause, failure to produce specific antibodies after MSH2017_2016_08_12:Heterogeneous group of immunodeficiency syndromes characterized by hypogammaglobulinemia of most isotypes, variable B-cell defects, and the presence of recurrent bacterial infections.NCI2016_NICHD_1602D:Abnormally low level of functional immunoglobulins in the blood that is not associated with a primary immunodeficiency.|NCI2016_02D:A primary immunodeficiency characterized by low levels or absence of all the immunoglobulin classes and lack of B-lymphocytes or plasma cells. It results in recurrent bacterial infections. Complications include autoimmune phenomena and cancer development.
Me Sh Disease Class
Immune System DiseasesImmune System Diseases; Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Immune System Diseases
Umls Semantic Type Name
Disease or Syndrome