DiseaseID 15244

扩张型心肌病伴羊毛发和角皮病

disease

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Interactive first-hop connections across herbs, ingredients, formulas, targets, diseases, symptoms, syndromes, evidence, and monographs.

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Disease: 1Formula: 11Herb: 12Symptom: 1Target: 18Links: 48
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Record Fields

Scalar fields from the final disease record.

Disease Id
15244
Core Entity Id
73151
Source Entity Count
1
Preferred Name
Cardiomyopathy Dilated With Woolly Hair And Keratoderma
Name Cn
扩张型心肌病伴羊毛发和角皮病
Name Pinyin
Kuo Zhang Xing Xin Ji Bing Ban Yang Mao Fa He Jiao Pi Bing
Name En
Cardiomyopathy Dilated With Woolly Hair And Keratoderma
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disgenet Type
disease
Mesh Class
Cardiovascular Diseases; Skin and Connective Tissue Diseases; Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Do Class
disease of anatomical entity
Hpo Class
Mesh Class Name
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases; Cardiovascular Diseases
Hpo Class Name
Do Class Name
disease of anatomical entity
Disease Definition
Version
v1
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Cardiomyopathy Dilated With Woolly Hair And Keratoderma
Role
preferred
Name
Cardiomyopathy, Dilated, With Woolly Hair, Keratoderma, And Tooth Agenesis
Role
preferred
Name
Cardiomyopathy, Dilated, With Woolly Hair And Keratoderma
Role
preferred
Name
Carvajal Syndrome
Role
alias
Name
DCWHKTA
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Herb
HBDIS017007HBDIS023018
Omim
605676615821
Umls
C1854063C4014393
Sym Map
SMDE00092SMDE01462
Do Class
DOID:7
Dis Ge Net
C1854063C4014393
Orphanet
65282
Umls Sty
T047
Me Sh Class
C14C16C17
Etcm Disease
Cardiomyopathy, Dilated, with Woolly Hair and KeratodermaCardiomyopathy, Dilated, with Woolly Hair, Keratoderma, and Tooth Agenesis
Tcmbank Disease
1296217707
Itcmdb Generated
ITX-DISEASE-B3F90657CE88ITX-DISEASE-D10BA64385DDITX-DISEASE-DAB38C109746

Attributes

Merged source attributes and domain-specific metadata.

Version
v1
Suppress
0
Page Title
Disease Cardiomyopathy, Dilated, with Woolly Hair and Keratoderma Details pageDisease Cardiomyopathy, Dilated, with Woolly Hair, Keratoderma, and Tooth Agenesis Details page
Do Class Name
disease of anatomical entity
Disease Type
disease
Do Disease Class
disease of anatomical entity
Umls Disease Type
Disease or Syndrome
Basic Information
Disease Name
Cardiomyopathy, Dilated, with Woolly Hair and Keratoderma
Global Category
Fetal diseases;Genetic diseases;Rare diseases
Anatomical Category
Cardiovascular diseases;Oral diseases;Skin diseases
Disease Name
Cardiomyopathy, Dilated, with Woolly Hair, Keratoderma, and Tooth Agenesis
Global Category
Genetic diseases
Anatomical Category
Cardiovascular diseases;Skin diseases
Me Sh Disease Class
Cardiovascular Diseases; Skin and Connective Tissue Diseases; Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases; Cardiovascular Diseases
Umls Semantic Type Name
Disease or Syndrome