DiseaseID 17279

常染色体显性遗传Emery-Dreifuss肌营养不良5型

disease

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Relationship Network

Interactive first-hop connections across herbs, ingredients, formulas, targets, diseases, symptoms, syndromes, evidence, and monographs.

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Disease: 1Formula: 7Herb: 12Symptom: 1Target: 17Links: 44
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Record Fields

Scalar fields from the final disease record.

Disease Id
17279
Core Entity Id
75487
Source Entity Count
1
Preferred Name
Emery-Dreifuss Muscular Dystrophy 5, Autosomal Dominant
Name Cn
常染色体显性遗传Emery-Dreifuss肌营养不良5型
Name Pinyin
Chang Ran Se Ti Xian Xing Yi Chuan Emery-dreifuss Ji Ying Yang Bu Liang 5 Xing
Name En
Emery-Dreifuss Muscular Dystrophy 5, Autosomal Dominant
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disgenet Type
disease
Mesh Class
Do Class
disease of anatomical entity; genetic disease
Hpo Class
Mesh Class Name
Hpo Class Name
Do Class Name
genetic disease; disease of anatomical entity
Disease Definition
Version
v1,v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Emery-Dreifuss Muscular Dystrophy 5, Autosomal Dominant
Role
preferred
Name
Autosomal Dominant Emery-Dreifuss Muscular Dystrophy 5
Role
alias
Name
EDMD5
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Herb
HBDIS019971
Omim
612999
Umls
C2751805
Sym Map
SMDE03039
Do Class
DOID:630DOID:7
Dis Ge Net
C2751805
Umls Sty
T047
Etcm Disease
Emery-Dreifuss Muscular Dystrophy 5, Autosomal Dominant
Tcmbank Disease
27191
Itcmdb Generated
ITX-DISEASE-6F88D42864A8

Attributes

Merged source attributes and domain-specific metadata.

Version
v1,v2
Suppress
0
Page Title
Disease Emery-Dreifuss Muscular Dystrophy 5, Autosomal Dominant Details page
Do Class Name
genetic disease; disease of anatomical entity
Disease Type
disease
Do Disease Class
disease of anatomical entity; genetic disease
Umls Disease Type
Disease or Syndrome
Basic Information
Disease Name
Emery-Dreifuss Muscular Dystrophy 5, Autosomal Dominant
Global Category
Genetic diseases;Rare diseases
Anatomical Category
Bone diseases;Cardiovascular diseases;Muscle diseases;Neuronal diseases
Dis Ge Net Disease Type
disease
Umls Semantic Type Name
Disease or Syndrome