DiseaseID 150

少毛症-淋巴水肿-毛细血管扩张综合征

disease

Hypotrichosis - lymphedema - telangiectasia is an extremely rare syndromic lymphedema disorder characterized by early-onset hypotrichosis, childhood-onset lymphedema, and variable telangiectasia, part

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Disease: 1Herb: 3Symptom: 2Target: 19Links: 29
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Record Fields

Scalar fields from the final disease record.

Disease Id
150
Core Entity Id
170
Source Entity Count
1
Preferred Name
Hypotrichosis-Lymphedema-Telangiectasia Syndrome
Name Cn
少毛症-淋巴水肿-毛细血管扩张综合征
Name Pinyin
Shao Mao Zheng - Lin Ba Shui Zhong - Mao Xi Xue Guan Kuo Zhang Zong He Zheng
Name En
Hypotrichosis-Lymphedema-Telangiectasia Syndrome
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disgenet Type
disease
Mesh Class
Cardiovascular Diseases; Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases
Do Class
genetic disease
Hpo Class
Mesh Class Name
Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases; Cardiovascular Diseases
Hpo Class Name
Do Class Name
genetic disease
Disease Definition
Hypotrichosis - lymphedema - telangiectasia is an extremely rare syndromic lymphedema disorder characterized by early-onset hypotrichosis, childhood-onset lymphedema, and variable telangiectasia, part
Version
v1,v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Hypotrichosis-Lymphedema-Telangiectasia Syndrome
Role
preferred
Name
Hypotrichosis-Lymphedema-Telangiectasia-Renal Defect Syndrome
Role
preferred
Name
Hypotrichosis, Lymphedema, Telangiectasia, Renal Defect Syndrome
Role
preferred
Name
GLOMERULONEPHRITIS WITH SPARSE HAIR AND TELANGIECTASES
Role
alias
Name
HLTRS
Role
alias
Name
HLTS
Role
alias
Name
Hypotrichosis-lymphedema-telangiectasia-membranoproliferative Glomerulonephritis Syndrome
Role
alias
Name
TELANGIECTATIC MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Herb
HBDIS015986HBDIS026440
Omim
137940607823
Umls
C1841989C1843004
Sym Map
SMDE03931SMDE05199
Do Class
DOID:630
Dis Ge Net
C1843004C4317151
Orphanet
69735
Umls Sty
T047
Me Sh Class
C14C15C17
Etcm Disease
Hypotrichosis-Lymphedema-Telangiectasia SyndromeHypotrichosis-Lymphedema-Telangiectasia-Renal Defect Syndrome
Tcmbank Disease
126335516
Itcmdb Generated
ITX-DISEASE-73B5F678470DITX-DISEASE-D737220F0968

Attributes

Merged source attributes and domain-specific metadata.

Version
v1,v2
Suppress
0
Page Title
Disease Hypotrichosis-Lymphedema-Telangiectasia Syndrome Details pageDisease Hypotrichosis-Lymphedema-Telangiectasia-Renal Defect Syndrome Details page
Do Class Name
genetic disease
Disease Type
disease
Do Disease Class
genetic disease
Umls Disease Type
Disease or Syndrome
Basic Information
Disease Name
Hypotrichosis-Lymphedema-Telangiectasia Syndrome
Global Category
Genetic diseases;Rare diseases
Anatomical Category
Immune diseases;Nephrological diseases
Disease Name
Hypotrichosis-Lymphedema-Telangiectasia-Renal Defect Syndrome
Global Category
Fetal diseases;Genetic diseases;Rare diseases
Anatomical Category
Cardiovascular diseases;Immune diseases;Nephrological diseases;Skin diseases
Disease Definition
Hypotrichosis - lymphedema - telangiectasia is an extremely rare syndromic lymphedema disorder characterized by early-onset hypotrichosis, childhood-onset lymphedema, and variable telangiectasia, part
Me Sh Disease Class
Cardiovascular Diseases; Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases; Cardiovascular Diseases
Umls Semantic Type Name
Disease or Syndrome