DiseaseID 9937

伴低或正常B细胞数的严重联合免疫缺陷

disease

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Disease: 1Symptom: 3Target: 5Links: 8
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Record Fields

Scalar fields from the final disease record.

Disease Id
9937
Core Entity Id
67077
Source Entity Count
1
Preferred Name
Severe Combined Immunodeficiency With Low Or Normal B-Cell Numbers
Name Cn
伴低或正常B细胞数的严重联合免疫缺陷
Name Pinyin
Ban Di Huo Zheng Chang B Xi Bao Shu De Yan Zhong Lian He Mian Yi Que Xian
Name En
Severe Combined Immunodeficiency With Low Or Normal B-Cell Numbers
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disgenet Type
disease
Mesh Class
Immune System Diseases; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Do Class
disease of anatomical entity; genetic disease
Hpo Class
Mesh Class Name
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Immune System Diseases
Hpo Class Name
Do Class Name
genetic disease; disease of anatomical entity
Disease Definition
Version
v1,v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Severe Combined Immunodeficiency With Low Or Normal B-Cell Numbers
Role
preferred
Name
Severe Combined Immunodeficiency, Autosomal Recessive, T Cell-Negative, B Cell-Positive, Nk Cell-Positive
Role
preferred
Name
Severe Combined Immunodeficiency, Autosomal Recessive, T Cell Negative, B Cell Positive, NK Cell Positive
Role
preferred
Name
SCID, AUTOSOMAL RECESSIVE, T CELL-NEGATIVE, B CELL-POSITIVE, NK CELL-POSITIVE
Role
alias
Name
Severe Combined Immunodeficiency [Scid] With Low Or Normal B-Cell Numbers
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Herb
HBDIS009499HBDIS015515
Omim
608971
Umls
C1837028
Icd10
D81.2
Sym Map
SMDE00140
Do Class
DOID:630DOID:7
Dis Ge Net
C0451694C1837028
Umls Sty
T047
Me Sh Class
C16C18C20
Tcmbank Disease
43566751

Attributes

Merged source attributes and domain-specific metadata.

Version
v1,v2
Suppress
0
Do Class Name
genetic disease; disease of anatomical entity
Disease Type
disease
Do Disease Class
disease of anatomical entity; genetic disease
Umls Disease Type
Disease or Syndrome
Me Sh Disease Class
Immune System Diseases; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Immune System Diseases
Umls Semantic Type Name
Disease or Syndrome