DiseaseID 8933
低补体血症性荨麻疹性血管炎
disease
Hypocomplementemic urticarial vasculitis (HUV) is an immune complex-mediated small vessel vasculitis characterized by urticaria and hypocomplementemia (low C1q with or without low C3 and C4), and usua
Relationship Network
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Disease: 1Formula: 2Symptom: 12Target: 17Links: 38
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Record Fields
Scalar fields from the final disease record.
- Disease Id
- 8933
- Core Entity Id
- 65934
- Source Entity Count
- 1
- Preferred Name
- Hypocomplementemic Urticarial Vasculitis
- Name Cn
- 低补体血症性荨麻疹性血管炎
- Name Pinyin
- Di Bu Ti Xue Zheng Xing Xun Ma Zhen Xing Xue Guan Yan
- Name En
- Hypocomplementemic Urticarial Vasculitis
- Name Latin
- Bilingual Status
- complete
- Disease Type
- disease
- Umls Disease Type
- Disease or Syndrome
- Disgenet Type
- disease
- Mesh Class
- Do Class
- Hpo Class
- Mesh Class Name
- Hpo Class Name
- Do Class Name
- Disease Definition
- Hypocomplementemic urticarial vasculitis (HUV) is an immune complex-mediated small vessel vasculitis characterized by urticaria and hypocomplementemia (low C1q with or without low C3 and C4), and usua
- Version
- v1,v2
- Suppressed
- No
Names
Preferred names, aliases, and source labels retained in the final schema.
Name
Hypocomplementemic Urticarial Vasculitis
Role
preferred
Name
Anti-C1q Vasculitis
Role
alias
Name
Mac Duffie Hypocomplementemic Urticarial Vasculitis
Role
alias
Name
Mac Duffie Syndrome
Role
alias
Name
McDuffie Hypocomplementemic Urticarial Vasculitis
Role
alias
Name
McDuffie Syndrome
Role
alias
Cross References
Trusted external identifiers retained for this final record.
Herb
HBDIS008137
Umls
C0343206
Icd10
M31.8
Sym Map
SMDE04828
Dis Ge Net
C0343206
Orphanet
36412
Umls Sty
T047
Etcm Disease
Hypocomplementemic Urticarial Vasculitis
Tcmbank Disease
25878
Itcmdb Generated
ITX-DISEASE-1D2D885B04B3ITX-DISEASE-DB3C6F873F5E
Attributes
Merged source attributes and domain-specific metadata.
Version
v1,v2
Suppress
0
Page Title
Disease Hypocomplementemic Urticarial Vasculitis Details page
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Basic Information
Disease Name
Hypocomplementemic Urticarial Vasculitis
Global Category
Rare diseases
Anatomical Category
Bone diseases;Cardiovascular diseases;Nephrological diseases
Disease Definition
Hypocomplementemic urticarial vasculitis (HUV) is an immune complex-mediated small vessel vasculitis characterized by urticaria and hypocomplementemia (low C1q with or without low C3 and C4), and usua
Dis Ge Net Disease Type
disease
Umls Semantic Type Name
Disease or Syndrome