Relationship Network
Interactive first-hop connections across herbs, ingredients, formulas, targets, diseases, symptoms, syndromes, evidence, and monographs.
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Disease: 1Target: 17Links: 24
Arranging relationship network...
Record Fields
Scalar fields from the final disease record.
- Disease Id
- 7863
- Core Entity Id
- 64730
- Source Entity Count
- 1
- Preferred Name
- Kininogen Deficiency, Total
- Name Cn
- 激肽原完全缺乏症
- Name Pinyin
- Ji Tai Yuan Wan Quan Que Fa Zheng
- Name En
- Kininogen Deficiency, Total
- Name Latin
- Bilingual Status
- complete
- Disease Type
- disease
- Umls Disease Type
- Disease or Syndrome
- Disgenet Type
- disease
- Mesh Class
- Hemic and Lymphatic Diseases
- Do Class
- Hpo Class
- Abnormality of metabolism/homeostasis; Abnormality of blood and blood-forming tissues
- Mesh Class Name
- Hemic and Lymphatic Diseases
- Hpo Class Name
- Abnormality of metabolism/homeostasis; Abnormality of blood and blood-forming tissues
- Do Class Name
- Disease Definition
- Version
- Suppressed
Names
Preferred names, aliases, and source labels retained in the final schema.
Name
Kininogen Deficiency, Total
Role
preferred
Name
High Molecular Weight Kininogen Deficiency
Role
preferred
Name
Fitzgerald Factor Deficiency
Role
alias
Name
Flaujeac Factor Deficiency
Role
alias
Name
Kininogen Deficiency
Role
alias
Name
Kininogen Deficiency, High Molecular Weight
Role
alias
Name
Reduced Kininogen Activity
Role
alias
Name
Williams Factor Deficiency
Role
alias
Name
Williams-Fitzgerald-Flaujeac Factor Deficiency
Role
alias
Cross References
Trusted external identifiers retained for this final record.
Hpo
HP:0005527
Herb
HBDIS006768HBDIS017330
Omim
228960
Dis Ge Net
C0272340C1856719
Umls Sty
T047
Hpo Class
HP:0001871HP:0001939
Me Sh Class
C15
Etcm Disease
High Molecular Weight Kininogen Deficiency
Tcmbank Disease
1132625565
Itcmdb Generated
ITX-DISEASE-ADA869BD8041
Attributes
Merged source attributes and domain-specific metadata.
Page Title
Disease High Molecular Weight Kininogen Deficiency Details page
Disease Type
disease
Hpo Class Name
Abnormality of metabolism/homeostasis; Abnormality of blood and blood-forming tissues
Hpo Disease Class
Abnormality of metabolism/homeostasis; Abnormality of blood and blood-forming tissues
Umls Disease Type
Disease or Syndrome
Basic Information
Disease Name
High Molecular Weight Kininogen Deficiency
Global Category
Genetic diseases;Rare diseases
Anatomical Category
Blood diseases
Me Sh Disease Class
Hemic and Lymphatic Diseases
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Hemic and Lymphatic Diseases
Umls Semantic Type Name
Disease or Syndrome