ITCMDBv1
DiseaseID 6231

肺泡状软组织肉瘤

disease

NCI2016_NCI-GLOSS_1602D:A soft tissue tumor that is most common in older children and teenagers. It begins in the soft supporting tissue that connects and surrounds the organs and other tissues. Alveolar soft part sarcom

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Disease: 1Herb: 1Symptom: 1Target: 19Links: 26
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Record Fields

Scalar fields from the final disease record.

Disease Id
6231
Core Entity Id
62853
Source Entity Count
1
Preferred Name
Alveolar Soft Part Sarcoma
Name Cn
肺泡状软组织肉瘤
Name Pinyin
Fei Pao Zhuang Ruan Zu Zhi Rou Liu
Name En
Alveolar Soft Part Sarcoma
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Neoplastic Process
Disgenet Type
disease
Mesh Class
Neoplasms
Do Class
disease of anatomical entity; disease of cellular proliferation
Hpo Class
Neoplasm
Mesh Class Name
Neoplasms
Hpo Class Name
Neoplasm
Do Class Name
disease of anatomical entity; disease of cellular proliferation
Disease Definition
NCI2016_NCI-GLOSS_1602D:A soft tissue tumor that is most common in older children and teenagers. It begins in the soft supporting tissue that connects and surrounds the organs and other tissues. Alveolar soft part sarcoma usually occurs in the legs, but can also occur in the arms, hands, head, or neck. It can cause the growth of new blood vessels that help the tumor grow and spread.|NCI2016_02D:A rare malignant neoplasm characterized by the presence of large epithelioid cells with abundant cytoplasm forming nests and pseudoalveolar structures. The groups of the epithelioid cells are separated by thin-walled sinusoidal spaces. It occurs most often in adolescents and young adults. In adults the most common sites of involvement are the extremities, and in infants and children, the head and neck. It usually presents as a slowly growing mass and it frequently metastasizes to other anatomic sites. The most common sites of metastasis are the lungs, bone, and brain.|MSH2017_2016_08_12:A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years of age. It appears in the muscles of the extremities in adults and most commonly in the head and neck regions of children. Though slow-growing, it commonly metastasizes to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1365)|HPO2016_07_04:A type of soft tissue sarcoma with a histological appearance reminiscent of alveoli because of its reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. [HPO:probinson, pmid:11244503]
Version
v1,v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Alveolar Soft Part Sarcoma
Role
preferred
Name
Adult Alveolar Soft Part Sarcoma
Role
preferred
Name
Childhood Alveolar Soft Part Sarcoma
Role
preferred
Name
ASPS
Role
alias
Name
Sarcoma, Alveolar Soft Part
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Hpo
HP:0012218
Herb
HBDIS004399HBDIS007066HBDIS007142
Me Sh
D018234
Omim
606243
Umls
C0206657
Sym Map
SMDE00299
Do Class
DOID:14566DOID:7
Dis Ge Net
C0206657C0279544C0279985
Umls Sty
T191
Hpo Class
HP:0002664
Me Sh Class
C04
Etcm Disease
Alveolar Soft Part Sarcoma
Tcmbank Disease
2609127058307606720
Itcmdb Generated
ITX-DISEASE-30D077D0D41FITX-DISEASE-49F941A08D56

Attributes

Merged source attributes and domain-specific metadata.

Version
v1,v2
Suppress
0
Page Title
Disease Alveolar Soft Part Sarcoma Details page
Do Class Name
disease of anatomical entity; disease of cellular proliferation
Disease Type
disease
Hpo Class Name
Neoplasm
Do Disease Class
disease of anatomical entity; disease of cellular proliferation
Hpo Disease Class
Neoplasm
Umls Disease Type
Neoplastic Process
Basic Information
Disease Name
Alveolar Soft Part Sarcoma
Global Category
Cancer diseases;Genetic diseases;Rare diseases
Anatomical Category
Muscle diseases
Disease Definition
NCI2016_NCI-GLOSS_1602D:A soft tissue tumor that is most common in older children and teenagers. It begins in the soft supporting tissue that connects and surrounds the organs and other tissues. Alveolar soft part sarcoma usually occurs in the legs, but can also occur in the arms, hands, head, or neck. It can cause the growth of new blood vessels that help the tumor grow and spread.|NCI2016_02D:A rare malignant neoplasm characterized by the presence of large epithelioid cells with abundant cytoplasm forming nests and pseudoalveolar structures. The groups of the epithelioid cells are separated by thin-walled sinusoidal spaces. It occurs most often in adolescents and young adults. In adults the most common sites of involvement are the extremities, and in infants and children, the head and neck. It usually presents as a slowly growing mass and it frequently metastasizes to other anatomic sites. The most common sites of metastasis are the lungs, bone, and brain.|MSH2017_2016_08_12:A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years of age. It appears in the muscles of the extremities in adults and most commonly in the head and neck regions of children. Though slow-growing, it commonly metastasizes to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1365)|HPO2016_07_04:A type of soft tissue sarcoma with a histological appearance reminiscent of alveoli because of its reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. [HPO:probinson, pmid:11244503]
Me Sh Disease Class
Neoplasms
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Neoplasms
Umls Semantic Type Name
Neoplastic Process