DiseaseID 4097

VIII型糖原贮积病

disease

MSH2017_2016_08_12:An x-linked recessive hepatic glycogen storage disease resulting from lack of expression of phosphorylase-b-kinase activity. Symptoms are relatively mild; hepatomegaly, increased liver glycogen, and de

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Disease: 1Symptom: 2Target: 1Links: 3
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Record Fields

Scalar fields from the final disease record.

Disease Id
4097
Core Entity Id
60393
Source Entity Count
1
Preferred Name
Glycogen Storage Disease Type Viii
Name Cn
VIII型糖原贮积病
Name Pinyin
Viii Xing Tang Yuan Zhu Ji Bing
Name En
Glycogen Storage Disease Type Viii
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disgenet Type
disease
Mesh Class
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Do Class
genetic disease; disease of metabolism
Hpo Class
Mesh Class Name
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Hpo Class Name
Do Class Name
disease of metabolism; genetic disease
Disease Definition
MSH2017_2016_08_12:An x-linked recessive hepatic glycogen storage disease resulting from lack of expression of phosphorylase-b-kinase activity. Symptoms are relatively mild; hepatomegaly, increased liver glycogen, and decreased leukocyte phosphorylase are present. Liver shrinkage occurs in response to glucagon.|CSP2006:x-linked recessive hepatic glycogen storage disease resulting from lack of expression of phosphorylase-b-kinase activity; symptoms are relatively mild, hepatomegaly, increased liver glycogen, and decreased leukocyte phosphorylase are present; liver shrinkage occurs in response to glucagon.
Version
v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Glycogen Storage Disease Type Viii
Role
preferred
Name
Glycogen Storage Disease Viii
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Herb
HBDIS001196
Me Sh
D006015
Umls
C0017927
Sym Map
SMDE09084
Do Class
DOID:0014667DOID:630
Dis Ge Net
C0017927
Umls Sty
T047
Me Sh Class
C16C18
Tcmbank Disease
23445

Attributes

Merged source attributes and domain-specific metadata.

Version
v2
Suppress
0
Do Class Name
disease of metabolism; genetic disease
Disease Type
disease
Do Disease Class
genetic disease; disease of metabolism
Umls Disease Type
Disease or Syndrome
Disease Definition
MSH2017_2016_08_12:An x-linked recessive hepatic glycogen storage disease resulting from lack of expression of phosphorylase-b-kinase activity. Symptoms are relatively mild; hepatomegaly, increased liver glycogen, and decreased leukocyte phosphorylase are present. Liver shrinkage occurs in response to glucagon.|CSP2006:x-linked recessive hepatic glycogen storage disease resulting from lack of expression of phosphorylase-b-kinase activity; symptoms are relatively mild, hepatomegaly, increased liver glycogen, and decreased leukocyte phosphorylase are present; liver shrinkage occurs in response to glucagon.
Me Sh Disease Class
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Umls Semantic Type Name
Disease or Syndrome