DiseaseID 26500

Hermansky-Pudlak综合征1型

Hermansky-Pudlak Syndrome 1

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Relationship Network

Interactive first-hop connections across herbs, ingredients, formulas, targets, diseases, symptoms, syndromes, evidence, and monographs.

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Disease: 1Symptom: 12Target: 17Links: 36
Arranging relationship network...

Record Fields

Scalar fields from the final disease record.

Disease Id
26500
Core Entity Id
119068
Source Entity Count
1
Preferred Name
Hermansky-Pudlak Syndrome 1
Name Cn
Hermansky-Pudlak综合征1型
Name Pinyin
Hermansky-pudlak Zong He Zheng 1 Xing
Name En
Hermansky-Pudlak Syndrome 1
Name Latin
Bilingual Status
complete
Disease Type
Umls Disease Type
Disgenet Type
Mesh Class
Do Class
Hpo Class
Mesh Class Name
Hpo Class Name
Do Class Name
Disease Definition
Version
v1,v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Hermansky-Pudlak Syndrome 1
Role
preferred

Cross References

Trusted external identifiers retained for this final record.

Umls
C2931875
Sym Map
SMDE03771
Etcm Disease
Hermansky-Pudlak Syndrome 1
Itcmdb Generated
ITX-DISEASE-56DEC37375C0

Attributes

Merged source attributes and domain-specific metadata.

Version
v1,v2
Suppress
0
Page Title
Disease Hermansky-Pudlak Syndrome 1 Details page
Basic Information
Disease Name
Hermansky-Pudlak Syndrome 1
Global Category
Genetic diseases;Metabolic diseases;Rare diseases
Anatomical Category
Blood diseases;Eye diseases;Immune diseases;Neuronal diseases;Skin diseases