DiseaseID 26369

短肋胸廓发育不良6型伴或不伴多指(趾)

Short-Rib Thoracic Dysplasia 6 With Or Without Polydactyly

NCI2016_02D:A group of rare, autosomal recessive inherited disorders characterized by a constricted thoracic cage, short ribs, and a 'trident' appearance of the acetabular roof. Polydactyly may or may not be present. Oth

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Disease: 1Symptom: 1Target: 12Links: 13
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Record Fields

Scalar fields from the final disease record.

Disease Id
26369
Core Entity Id
118937
Source Entity Count
1
Preferred Name
Short-Rib Thoracic Dysplasia 6 With Or Without Polydactyly
Name Cn
短肋胸廓发育不良6型伴或不伴多指(趾)
Name Pinyin
Duan Le Xiong Kuo Fa Yu Bu Liang 6 Xing Ban Huo Bu Ban Duo Zhi ( Zhi )
Name En
Short-Rib Thoracic Dysplasia 6 With Or Without Polydactyly
Name Latin
Bilingual Status
complete
Disease Type
Umls Disease Type
Disgenet Type
Mesh Class
Do Class
Hpo Class
Mesh Class Name
Hpo Class Name
Do Class Name
Disease Definition
NCI2016_02D:A group of rare, autosomal recessive inherited disorders characterized by a constricted thoracic cage, short ribs, and a 'trident' appearance of the acetabular roof. Polydactyly may or may not be present. Other abnormalities include cleft lip and palate and abnormalities of the brain, eye, heart, liver, pancreas, intestine, kidney, and genitalia.
Version
v1,v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Short-Rib Thoracic Dysplasia 6 With Or Without Polydactyly
Role
preferred
Source
SymMap_v2
Preferred
Yes

Cross References

Trusted external identifiers retained for this final record.

Umls
C0024507
Sym Map
SMDE03140

Attributes

Merged source attributes and domain-specific metadata.

Version
v1,v2
Suppress
0
Disease Definition
NCI2016_02D:A group of rare, autosomal recessive inherited disorders characterized by a constricted thoracic cage, short ribs, and a 'trident' appearance of the acetabular roof. Polydactyly may or may not be present. Other abnormalities include cleft lip and palate and abnormalities of the brain, eye, heart, liver, pancreas, intestine, kidney, and genitalia.