DiseaseID 26175
肺泡毛细血管发育不良伴肺静脉错位
Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins
NCI2016_NICHD_1602D:A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus.|NC
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Disease: 1Formula: 9Herb: 1Symptom: 2Target: 20Links: 36
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Record Fields
Scalar fields from the final disease record.
- Disease Id
- 26175
- Core Entity Id
- 118743
- Source Entity Count
- 1
- Preferred Name
- Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins
- Name Cn
- 肺泡毛细血管发育不良伴肺静脉错位
- Name Pinyin
- Fei Pao Mao Xi Xue Guan Fa Yu Bu Liang Ban Fei Jing Mai Cuo Wei
- Name En
- Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins
- Name Latin
- Bilingual Status
- complete
- Disease Type
- Umls Disease Type
- Disgenet Type
- Mesh Class
- Do Class
- Hpo Class
- Mesh Class Name
- Hpo Class Name
- Do Class Name
- Disease Definition
- NCI2016_NICHD_1602D:A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus.|NCI2016_02D:A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus.(NICHD)|MSH2017_2016_08_12:A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT).|HPO2016_07_04:Systemic desaturation of a liveborn baby resulting from persistent pulmonary hypertension with a patent ductus arteriosus and patent foramen ovale, such that the circulation in postnatal life follows the fetal course. [DDD:dbrown]
- Version
- v1,v2
- Suppressed
- No
Names
Preferred names, aliases, and source labels retained in the final schema.
Name
Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins
Role
preferred
Cross References
Trusted external identifiers retained for this final record.
Umls
C0031190
Sym Map
SMDE02302
Etcm Disease
Alveolar Capillary Dysplasia with Misalignment of Pulmonary Veins
Itcmdb Generated
ITX-DISEASE-37ADD4AE9E1A
Attributes
Merged source attributes and domain-specific metadata.
Version
v1,v2
Suppress
0
Page Title
Disease Alveolar Capillary Dysplasia with Misalignment of Pulmonary Veins Details page
Basic Information
Disease Name
Alveolar Capillary Dysplasia with Misalignment of Pulmonary Veins
Global Category
Genetic diseases;Rare diseases
Anatomical Category
Respiratory diseases
Disease Definition
NCI2016_NICHD_1602D:A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus.|NCI2016_02D:A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus.(NICHD)|MSH2017_2016_08_12:A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT).|HPO2016_07_04:Systemic desaturation of a liveborn baby resulting from persistent pulmonary hypertension with a patent ductus arteriosus and patent foramen ovale, such that the circulation in postnatal life follows the fetal course. [DDD:dbrown]