DiseaseID 26121

完全性雄激素不敏感综合征

Complete Androgen Insensitivity Syndrome

Complete androgen insensitivity syndrome (CAIS) is a form of androgen insensitivity syndrome (AIS; see this term), a disorder of sex development (DSD), characterized by the presence of female external

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Disease: 1Symptom: 1Target: 16Links: 25
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Record Fields

Scalar fields from the final disease record.

Disease Id
26121
Core Entity Id
118689
Source Entity Count
1
Preferred Name
Complete Androgen Insensitivity Syndrome
Name Cn
完全性雄激素不敏感综合征
Name Pinyin
Wan Quan Xing Xiong Ji Su Bu Min Gan Zong He Zheng
Name En
Complete Androgen Insensitivity Syndrome
Name Latin
Bilingual Status
complete
Disease Type
Umls Disease Type
Disgenet Type
Mesh Class
Do Class
Hpo Class
Mesh Class Name
Hpo Class Name
Do Class Name
Disease Definition
Complete androgen insensitivity syndrome (CAIS) is a form of androgen insensitivity syndrome (AIS; see this term), a disorder of sex development (DSD), characterized by the presence of female external
Version
v1
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Complete Androgen Insensitivity Syndrome
Role
preferred

Cross References

Trusted external identifiers retained for this final record.

Omim
300274
Sym Map
SMDE02009
Orphanet
99429
Etcm Disease
Complete Androgen Insensitivity Syndrome
Itcmdb Generated
ITX-DISEASE-87D34738EB13

Attributes

Merged source attributes and domain-specific metadata.

Version
v1
Suppress
0
Page Title
Disease Complete Androgen Insensitivity Syndrome Details page
Basic Information
Disease Name
Complete Androgen Insensitivity Syndrome
Global Category
Fetal diseases;Rare diseases
Anatomical Category
Endocrine diseases;Reproductive diseases
Disease Definition
Complete androgen insensitivity syndrome (CAIS) is a form of androgen insensitivity syndrome (AIS; see this term), a disorder of sex development (DSD), characterized by the presence of female external