DiseaseID 14464

Hermansky-Pudlak综合征2型

disease

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Relationship Network

Interactive first-hop connections across herbs, ingredients, formulas, targets, diseases, symptoms, syndromes, evidence, and monographs.

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Disease: 1Symptom: 7Target: 18Links: 31
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Record Fields

Scalar fields from the final disease record.

Disease Id
14464
Core Entity Id
72253
Source Entity Count
1
Preferred Name
Hermansky-Pudlak Syndrome 2
Name Cn
Hermansky-Pudlak综合征2型
Name Pinyin
Hermansky-pudlak Zong He Zheng 2 Xing
Name En
Hermansky-Pudlak Syndrome 2
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disgenet Type
disease
Mesh Class
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Eye Diseases; Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases
Do Class
genetic disease
Hpo Class
Mesh Class Name
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Eye Diseases; Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases
Hpo Class Name
Do Class Name
genetic disease
Disease Definition
Version
v1,v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Hermansky-Pudlak Syndrome 2
Role
preferred
Name
HPS2
Role
alias
Name
Hermansky Pudlak Syndrome 2
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Herb
HBDIS015927
Omim
608233
Umls
C1842362
Sym Map
SMDE01999
Do Class
DOID:630
Dis Ge Net
C1842362
Umls Sty
T047
Me Sh Class
C11C15C16C17C18
Etcm Disease
Hermansky-Pudlak Syndrome 2
Tcmbank Disease
31847
Itcmdb Generated
ITX-DISEASE-9B2EBB3E7BC4

Attributes

Merged source attributes and domain-specific metadata.

Version
v1,v2
Suppress
0
Page Title
Disease Hermansky-Pudlak Syndrome 2 Details page
Do Class Name
genetic disease
Disease Type
disease
Do Disease Class
genetic disease
Umls Disease Type
Disease or Syndrome
Basic Information
Disease Name
Hermansky-Pudlak Syndrome 2
Global Category
Genetic diseases;Metabolic diseases;Rare diseases
Anatomical Category
Blood diseases;Eye diseases;Immune diseases;Neuronal diseases;Skin diseases
Me Sh Disease Class
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Eye Diseases; Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Eye Diseases; Skin and Connective Tissue Diseases; Hemic and Lymphatic Diseases
Umls Semantic Type Name
Disease or Syndrome