DiseaseID 13470

假性泽尔韦格综合征

disease

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Relationship Network

Interactive first-hop connections across herbs, ingredients, formulas, targets, diseases, symptoms, syndromes, evidence, and monographs.

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Disease: 1Symptom: 3Target: 6Links: 9
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Record Fields

Scalar fields from the final disease record.

Disease Id
13470
Core Entity Id
71114
Source Entity Count
1
Preferred Name
Pseudo-Zellweger Syndrome
Name Cn
假性泽尔韦格综合征
Name Pinyin
Jia Xing Ze Er Wei Ge Zong He Zheng
Name En
Pseudo-Zellweger Syndrome
Name Latin
Bilingual Status
complete
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disgenet Type
disease
Mesh Class
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic DiseasesFemale Urogenital Diseases and Pregnancy Complications; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Nervous System Diseases; Digestive System Diseases; Male Urogenital Diseases
Do Class
genetic disease
Hpo Class
Mesh Class Name
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Digestive System Diseases; Nutritional and Metabolic Diseases; Female Urogenital Diseases and Pregnancy Complications; Male Urogenital Diseases; Nervous System DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Hpo Class Name
Do Class Name
genetic disease
Disease Definition
Version
v2
Suppressed
No

Names

Preferred names, aliases, and source labels retained in the final schema.

Name
Pseudo-Zellweger Syndrome
Role
preferred
Name
Deficiency of Acetyl-Coa Acetyltransferase
Role
preferred
Name
3-Ketothiolase Deficiency
Role
alias
Name
Alpha-Methylacetoacetic Aciduria
Role
alias
Name
Alpha-Methylacetoaceticaciduria
Role
alias
Name
Beta-Ketothiolase Deficiency
Role
alias

Cross References

Trusted external identifiers retained for this final record.

Herb
HBDIS014499HBDIS014528
Omim
203750
Umls
C1533628
Sym Map
SMDE12511
Do Class
DOID:630
Dis Ge Net
C1533628C1536500
Umls Sty
T047
Me Sh Class
C06C10C12C13C16C18
Tcmbank Disease
1128123457

Attributes

Merged source attributes and domain-specific metadata.

Version
v2
Suppress
0
Do Class Name
genetic disease
Disease Type
disease
Do Disease Class
genetic disease
Umls Disease Type
Disease or Syndrome
Me Sh Disease Class
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic DiseasesFemale Urogenital Diseases and Pregnancy Complications; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases; Nervous System Diseases; Digestive System Diseases; Male Urogenital Diseases
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Digestive System Diseases; Nutritional and Metabolic Diseases; Female Urogenital Diseases and Pregnancy Complications; Male Urogenital Diseases; Nervous System DiseasesCongenital, Hereditary, and Neonatal Diseases and Abnormalities; Nutritional and Metabolic Diseases
Umls Semantic Type Name
Disease or Syndrome