DiseaseID 11939
巨噬细胞活化综合征
disease
NCI2016_NICHD_1602D:A potentially fatal complication of rheumatic disease characterized by fever, pancytopenia, hemophagocytosis, hyperferritinemia, liver insufficiency, coagulopathy and neurologic symptoms.|NCI2016_02D:
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Disease: 1Symptom: 1Target: 12Links: 13
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Record Fields
Scalar fields from the final disease record.
- Disease Id
- 11939
- Core Entity Id
- 69391
- Source Entity Count
- 1
- Preferred Name
- Macrophage Activation Syndrome
- Name Cn
- 巨噬细胞活化综合征
- Name Pinyin
- Ju Shi Xi Bao Huo Hua Zong He Zheng
- Name En
- Macrophage Activation Syndrome
- Name Latin
- Bilingual Status
- complete
- Disease Type
- disease
- Umls Disease Type
- Disease or Syndrome
- Disgenet Type
- disease
- Mesh Class
- Immune System Diseases
- Do Class
- Hpo Class
- Mesh Class Name
- Immune System Diseases
- Hpo Class Name
- Do Class Name
- Disease Definition
- NCI2016_NICHD_1602D:A potentially fatal complication of rheumatic disease characterized by fever, pancytopenia, hemophagocytosis, hyperferritinemia, liver insufficiency, coagulopathy and neurologic symptoms.|NCI2016_02D:A complication of rheumatic disease that is caused by excessive activation and uncontrolled proliferation of T lymphocytes and well-differentiated macrophages. It is characterized by fever, pancytopenia, liver insufficiency, coagulopathy and neurologic symptoms.(NICHD)|MSH2017_2016_08_12:A serious complication of childhood systemic inflammatory disorders that is thought to be caused by excessive activation and proliferation of T-LYMPHOCYTES and MACROPHAGES. It is seen predominantly in children with systemic onset JUVENILE IDIOPATHIC ARTHRITIS.
- Version
- v2
- Suppressed
- No
Names
Preferred names, aliases, and source labels retained in the final schema.
Name
Macrophage Activation Syndrome
Role
preferred
Cross References
Trusted external identifiers retained for this final record.
Herb
HBDIS012589
Me Sh
D055501
Umls
C1096155
Sym Map
SMDE10629
Dis Ge Net
C1096155
Umls Sty
T047
Me Sh Class
C20
Tcmbank Disease
29480
Attributes
Merged source attributes and domain-specific metadata.
Version
v2
Suppress
0
Disease Type
disease
Umls Disease Type
Disease or Syndrome
Disease Definition
NCI2016_NICHD_1602D:A potentially fatal complication of rheumatic disease characterized by fever, pancytopenia, hemophagocytosis, hyperferritinemia, liver insufficiency, coagulopathy and neurologic symptoms.|NCI2016_02D:A complication of rheumatic disease that is caused by excessive activation and uncontrolled proliferation of T lymphocytes and well-differentiated macrophages. It is characterized by fever, pancytopenia, liver insufficiency, coagulopathy and neurologic symptoms.(NICHD)|MSH2017_2016_08_12:A serious complication of childhood systemic inflammatory disorders that is thought to be caused by excessive activation and proliferation of T-LYMPHOCYTES and MACROPHAGES. It is seen predominantly in children with systemic onset JUVENILE IDIOPATHIC ARTHRITIS.
Me Sh Disease Class
Immune System Diseases
Dis Ge Net Disease Type
disease
Disease Class Name Me Sh
Immune System Diseases
Umls Semantic Type Name
Disease or Syndrome